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Linear and Whorled Nevoid Hypermelanosis in a Nigerian Child: A Case Report and Literature Review
Current Issue
Volume 5, 2017
Issue 5 (October)
Pages: 32-34   |   Vol. 5, No. 5, October 2017   |   Follow on         
Paper in PDF Downloads: 39   Since Aug. 28, 2017 Views: 976   Since Aug. 28, 2017
Authors
[1]
Ujuanbi Amenawon Susan, Department of Paediatrics, University of Port Harcourt Teaching Hospital, Port Harcourt City, Rivers State, Nigeria.
[2]
Eke Gracia, Department of Paediatrics, University of Port Harcourt Teaching Hospital, Port Harcourt City, Rivers State, Nigeria.
[3]
Akani Nwadiuto Afonne, Department of Paediatrics, University of Port Harcourt Teaching Hospital, Port Harcourt City, Rivers State, Nigeria.
Abstract
Linear and whorled nevoid hypermelanosis (LWNH) is a rare skin condition characterized by linear streaks and swirls of macular hyperpigmentation along the lines of Blaschko. The disease may occasionally have associated extracutaneous manifestations. The exact pathogenesis is unknown and no satisfactory treatment modalities for LWNH are currently available. There are few case reports of the disease in literature worldwide and none has been previously reported in Nigeria. We are reporting one such rare case of linear and whorled nevoid hypermelanosis in a 9 month old Nigerian child. We report a 9 month old female who presented with abnormal dark skin pigmentation noticed at birth suggestive of LWNH with extracutaneous presentation including microcephaly, turricephaly, anisocoria, nystagmus and delayed developmental milestones. This shows the existence of this rare disease in Nigeria. Linear and whorled nevoid hypermelanosis though uncommon, is associated with significant morbidity especially among those with extracutaneous lesions. No effective treatment is available for this disorder.
Keywords
Linear, Whorled, Nevoid, Hypermelanosis, Nigerian
Reference
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