2015 Persian Gulf Criteria for Early Diagnosis of Behcet’s Disease
Behcet’s disease (BD) is a chronic inflammatory multisystem disorder belongs to the vasculitides characterized by oral aphthosis, genital aphthosis, ocular inflammation, skin lesions and vascular involvement. Behcet’s disease typically affects young adults 20 to 40 years of age with no significant difference in gender. Oral aphthosis is classically recurrent and it can be multiple or major but less likely persistent. Genital aphthosis in men and external genital aphthosis in women can be replaced by scar after improvement. Ocular inflammation is including anterior uveitis, intermediate/posterior uveitis and retinal vasculitis. Skin lesions are including pseudofolliculitis, erythema nodosum, acneiform lesions, pustular lesions, pyoderma gangrenosum, dermal aphthosis, superficial thrombophlebitis and so on. Vascular involvements are including vasculitis of small, medium and large sized vessels, arterial and venous type. Hemorrhage, stenosis and especially aneurysm formation and thrombosis are all of the vascular features of this disorder. Initial presentations of BD are commonly Oral aphthosis, Genital aphthosis and eye lesions and sometimes skin lesions and articular involvement. There are 16 sets of classification criteria for this disease including International Study Group (ISG, 1990) criteria, International Criteria for Behcet’s Disease (ICBD, 2006), ICBD revised (ITR-ICBD, 2013) and etc., but we don’t have any criteria for early diagnosis of it. In this letter the corresponding author wants to deliver Persian Gulf criteria for early diagnosis of BD.
Behcet's Disease, ISG Criteria, ICBD Criteria, ICBD Revised Criteria, Persian Gulf Criteria
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